Angelman syndrome

Angelman syndrome
Other namesAngelman's syndrome
A five-year-old girl with Angelman syndrome. Features shown include telecanthus, bilateral epicanthic folds, small head, wide mouth, and an apparently happy demeanor; hands with tapered fingers, abnormal creases and broad thumbs.
Pronunciation
  • /ˈæŋɡəlmən/, /ˈænəlmən/, or /ˈnəlmən/
SpecialtyMedical genetics
SymptomsDelayed development, unusually happy, intellectual disability, limited to no functional speech, balance and movement problems, small head, seizures
Usual onsetNoticeable by 6–12 months
CausesGenetic (new mutation)
Diagnostic methodBased on symptoms, genetic testing
Differential diagnosisCerebral palsy, autism, Rett syndrome, Prader–Willi syndrome
TreatmentSupportive care
PrognosisNearly normal life expectancy
Frequency1 in 12,000 to 20,000 people

Angelman syndrome (AS) is a genetic disorder that affects approximately 1 in 15,000 individuals. AS impairs the function of the nervous system, producing symptoms, such as severe intellectual disability, developmental disability, limited to no functional speech, balance and movement problems, seizures, hyperactivity, and sleep problems. Physical symptoms include a small head and a specific facial appearance. Additionally, those affected usually have a happy personality and have a particular interest in water. Angelman syndrome involves genes that have also been linked to 1–2% of autism spectrum disorder cases.