Asplenia with cardiovascular anomalies

Asplenia with cardiovascular anomalies
Other namesIvemark syndrome
This condition is inherited in an autosomal recessive manner
SpecialtyMedical genetics 

Asplenia with cardiovascular anomalies, also known as Ivemark syndrome and right atrial isomerism, is an example of a heterotaxy syndrome. These uncommon congenital disorders are characterized by defects in the heart, spleen and paired organs such as the lungs and kidneys. Another name is "asplenia-cardiovascular defect-heterotaxy".

Right atrial isomerism is named for its discoverer, Swedish pathologist Biörn Ivemark.

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