Branchio-oto-renal syndrome

Branchio-oto-renal syndrome
Other namesBOR syndrome, Branchiootorenal syndrome
Branchio-oto-renal syndrome has an autosomal dominant pattern of inheritance.
SpecialtyMedical genetics 
SymptomsEar abnormalities
CausesMutations in genes, EYA1, SIX1, and SIX5
Diagnostic methodLaboratory test results, Physical exam
TreatmentBranchial fistula may need surgery

Branchio-oto-renal syndrome (BOR) is an autosomal dominant genetic disorder involving the kidneys, ears, and neck. It is also known as Melnick-Fraser syndrome.