Cartilage–hair hypoplasia

Cartilage-hair hypoplasia
Other namesMcKusick type metaphyseal chondrodysplasia:578
Cartilage-hair hypoplasia has an autosomal recessive pattern of inheritance
Pronunciation
  • /ˌkɑːrtɪlɪ...ˌhpˈplʒə/
SymptomsShort limb dwarfism
Very fine thin light hairs and eyebrows
Hyperextensible joints of hand and feet
Abnormalities of spine
Neutropenia
Defective antibody and cell mediated immunity

Cartilage–hair hypoplasia (CHH) is a rare genetic disorder. Symptoms may include short-limbed dwarfism due to skeletal dysplasia, variable level of immunodeficiency, and predisposition to cancer. It was first reported by Victor McKusick in 1965.