Congenital anosmia

Congenital Anosmia
Other namesIsolated Congenital Anosmia
Olfactory bulbs and olfactory tracts outlined in red. These structures, which are critical for the sense of smell, are missing or underdeveloped in individuals with congenital anosmia.
SpecialtyOtorhinolaryngology
SymptomsComplete inability to perceive smell from birth
ComplicationsSafety risks (e.g., inability to detect smoke or gas leaks), potential nutritional issues
Usual onsetBirth
DurationLifelong
TypesIsolated, Syndromic (e.g., Kallmann syndrome)
CausesGenetic mutations, developmental defects of the olfactory bulbs and tracts
Risk factorsGenetic predisposition
Diagnostic methodMedical history, physical examination, smell tests, brain imaging (MRI/CT), nasal endoscopy, olfactory nerve testing
Differential diagnosisAcquired anosmia, other olfactory disorders
PreventionNone
TreatmentNo cure; management includes safety precautions and coping strategies
MedicationNone
PrognosisLifelong condition with management of associated risks
FrequencyApproximately 1 in 10,000 individuals

Congenital anosmia is a rare condition characterized by the complete inability to perceive smell from birth. It affects approximately 1 in 10,000 individuals and is often diagnosed later in life due to its subtle presentation and lack of associated symptoms.