Koolen–De Vries syndrome

Koolen–De Vries syndrome
Other names17q21.31 microdeletion syndrome
Photo of the person with KdVS, with narrow and upslanted palpebral fissures, prominent ears and a pear-shaped nose.
SymptomsIntellectual disability, feeding problems, hypotonia
Usual onsetConception
DurationLifelong
CausesChromosomal microdeletion
Diagnostic methodFluorescence in situ hybridization

Koolen–De Vries syndrome (KdVS), also known as 17q21.31 microdeletion syndrome, is a rare genetic disorder caused by a deletion of a segment of chromosome 17 which contains six genes. This deletion syndrome was discovered independently in 2006 by three different research groups.