Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
| Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency | |
|---|---|
| Other names | LCHAD deficiency |
| Long-chain 3-hydroxyacyl-coenzyme; A dehydrogenase deficiency has an autosomal recessive pattern of inheritance. | |
Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting.