Methylcrotonyl-CoA carboxylase

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Structures	Swiss-model
Domains	InterPro

Methylcrotonoyl-coenzyme A carboxylase 1 (alpha)
Methylcrotonoyl-coenzyme A carboxylase 1 (alpha)
Identifiers
Symbol	MCCC1
NCBI gene	56922
HGNC	6936
OMIM	609010
RefSeq	NM_020166
UniProt	Q96RQ3
Other data
EC number	6.4.1.4
Locus	Chr. 3 q27.1
Structures
Search for
Structures	Swiss-model
Domains	InterPro

methylcrotonoyl-CoA carboxylase
Identifiers
Aliases	methylcrotonyl-CoA carboxylase3-methylcrotonoyl-CoA:carbon-dioxide ligase (ADP-forming)beta-methylcrotonyl coenzyme A carboxylaseMCCCmethylcrotonyl coenzyme A carboxylasebeta-methylcrotonyl CoA carboxylasebeta-methylcrotonyl-CoA carboxylase
External IDs	GeneCards: ; OMA:- orthologs
Orthologs
	n/a
	n/a
	n/a
	n/a
	n; a
	n/a
	n/a
	n/a
	n/a
	n/a
	Wikidata
View/Edit Human

Methylcrotonoyl-coenzyme A carboxylase 2 (beta)

Identifiers

Symbol

MCCC2

Other data

Chr. 5 q12-q13

Search for
Structures	Swiss-model
Domains	InterPro

Methylcrotonyl CoA carboxylase (EC 6.4.1.4, MCC) (3-methylcrotonyl CoA carboxylase, methylcrotonoyl-CoA carboxylase) is a biotin-requiring enzyme located in the mitochondria. MCC uses bicarbonate as a carboxyl group source to catalyze the carboxylation of a carbon adjacent to a carbonyl group performing the fourth step in processing leucine, an essential amino acid.