Osteopathia striata with cranial sclerosis

Osteopatgia striata with cranial stenosis
Other namesOSCS
SpecialtyMedical genetics, Radiology
SymptomsBone anomalies mainly
ComplicationsRespiratory arrest and nutritional deficiency
Usual onsetBirth
DurationLifelong
CausesGenetic mutation
Preventionnone
PrognosisMedium
Frequencyrare, between 70 and 90 cases have been described
Deaths

Osteopathia striata with cranial sclerosis (OSCS) is a rare genetic entity characterized by osseous abnormalities.