Prune belly syndrome

Prune belly syndrome
Other namesAbdominal muscle deficiency syndrome, congenital absence of the abdominal muscles, Eagle-Barrett syndrome, Obrinsky syndrome, Fröhlich syndrome, triad syndrome
Prune belly syndrome in an Egyptian child with Down syndrome.
SpecialtyMedical genetics 

Prune belly syndrome (PBS) is a rare, genetic birth defect affecting about 1 in 40,000 births. About 97% of those affected are male. Prune belly syndrome is a congenital disorder of the urinary system, characterized by a triad of symptoms. The syndrome is named for the mass of wrinkled skin that is often (but not always) present on the abdomen of those with the disorder.

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