Very long-chain acyl-coenzyme A dehydrogenase deficiency
| Very long-chain acyl-coenzyme A dehydrogenase deficiency | |
|---|---|
| Other names | VLCADD |
| Very long-chain acyl-coenzyme: A dehydrogenase deficiency has an autosomal recessive pattern of inheritance. | |
Very long-chain acyl-coenzyme A dehydrogenase deficiency is a fatty-acid metabolism disorder which prevents the body from converting certain fats to energy, particularly during periods without food.
Those affected by this disorder have inadequate levels of an enzyme that breaks down a group of fats called very long-chain fatty acids.